The associated cranial nerve palsies tend to be more cosmetic than debilitating. Glomus jugulare tumors grow on the jugular bulb, while glomus tympanicum tumors grow in the middle ear space. This tumour is classified as a perivascular tumour also pericytic tumour which is a subset of soft tissue tumours. A typical case of glomus jugulare tumor was presented. The complex anatomy of the region and the limited surgical techniques available discouraged a more hazardous approach, especially surgical resection of this highly haemorrhagic tumour. Background glomus jugulare tumors gjts are uncommon and locally disruptive tumors that usually arise within the jugular foramen of the temporal bone. The glomus jugulare tumor is a slowly growing benign neoplasm originating from neural crest. Management of glomus jugulare tumors requires a good knowledge of the temporal bone and cervical as well as intracranial anatomy to evaluate the extent and progression of the tumor and the type of surgical approach required.
Their natural history, surgical treatment, and outcome have been well addressed in the recent literature. Socalled glomus jugulare tumors gjts, also called paragangliomas or chemodectomas have their epicenter within the adventitia of the jugular bulb and. This tumor can affect the ear, upper neck, base of the skull, and the surrounding blood vessels and nerves. Tumor control and complications after stereotactic radiosurgery. Treatment of recurrent and residual glomus jugulare tumors. A definitive consensus on the best treatment modality for this disease cannot be reached because there are few studies and most of them lack adequate information. Glomus bodies, firstly described by stacy rufus guild in 1941, are part of the chemoreceptor system and composed of nonchromaffin epitheloid cells surrounded by a thin fibrous capsule embedded in a capillary network 1, 2. Glomus jugulare glomus jugulare tumours glomus jugulare tumor glomus yugullar tumors glomus jugulare paragangliomas.
Jensen, department of anesthesiology, university of iowa college of medicine, iowa city, iowa 52242. Paraganglioma, tumor cuerpo carotideo, glomus timpanico, glomus yugular, abordaje infratemporal. Glomus jugulare paraganglioma is a paraganglioma of the head and neck that is confined to the jugular fossa. Stereotactic radiosurgery for the treatment of glomus. The neuroradiological examination showed erosion of the petrous part of the right temporal bone, displacement of the right pontocerebellar cistern and dilatation of the ambiens cistern in the same side. Jan 25, 2020 glomus yugular pdf glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma. Epidemiology the relative prevalence of glomus jugulare wi. Because of the anatomic location of glomus jugulare, this tumor typically involves the seventh, ninth, tenth, and eleventh cranial nerves. Jan 07, 2016 glomus jugulare tumours tend to grow slowly with only a small proportion metastasising.
Current perspectives in the management of glomus jugulare. Glomus yugular timpanico pdf glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma. They are typically benign and are treated by surgical removal. The authors noted that familial carotid body tumors tended to be multiple. Glomus jugulare tumor information mount sinai new york. Tumor of the glomus jugulare with extension into the middle ear nonchromaffin paraganglioma or carotidbodytype tumor. They are rare tumors, with an overall estimated incidence of 0 000. The prognosis of these tumors is related to the anatomical location and size of the lesion. A glomus tumor is a rare neoplasm arising from the. A glomus jugulare tumor is a tumor within the skull cavity. Tumor del glomus yugular jugular glomus tumor youtube. Efficacy and safety of stereotactic radiosurgery for glomus jugulare tumors. They are considered as benign and slow growing tumors. In certain patients, residual tumor is left at surgery to prevent devastating lower cranial nerve deficits or to reduce potential morbidity associated with carotid artery injury.
Glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma a glomus tumor also known as a solitary glomus tumor, solid glomus tumor, is a rare neoplasm arising from the glomus body and mainly found under the nail, on the fingertip or in the foot. The temporal bones are on the sides of your skull, or your temples. Resection of a leftsided glomus jugulare tumor in a 21yearold lady using a lateral combined transmastoidtranscervical approach augmented by anterior fa. Glomus vagale tumor genetic and rare diseases information. A case of tumor of the glomus jugulare in a 57 years old patient in which the symptoms lasted four years is reported. Unlike other types of cancer, there is no test that determines benign from malignant tumors. Apr 20, 2014 tumor del glomus carotideo quemodectoma 1. A patient with a glomus jugulare often hears their own heart beat in the affected ear pulsatile tinnitus. For a long time, radiotherapy was the only treatment option available to otorhinolaryngologists to try to control glomus jugulare paragangliomas. While it is a rare tumor, it is the most common of the jugular fossa tumors. A case report a case of tumor of the glomus jugulare in a 57 years old patient in which the symptoms lasted four years is reported.
This distinction is important because the two types of tumor require. Tumors of the glomus jugulare are benign, slowgrowing paragangliomas. Glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma a glomus tumor also known as a solitary glomus tumor, solid glomus tumor, is a rare neoplasm arising from the glomus body and mainly found under the nail, on the fingertip or in the foot 670 they account for less than 2% of all soft tissue tumors. Radiosurgery play a relevant role as a therapeutic option in these tumors and its use has grown in popularity. Surgery of glomus jugulare tumors pubmed central pmc. Jugulo tympanic glomus tumors or paragangliomas originate from. Familial glomus jugulare tumors were likely described in 3 affected sisters reported in 1937 by goekoop cited by rosen, 1952.
Tumores glomus localizados en oido medio, mastoides y cerebro. Glomus jugulare tumor is a rare, benign paraganglioma of the skull base that forms in the jugular fossa of the temporal bone and is made up of glomus cells which are neural crest cell derivatives. The treatment of glomus jugulare tumors can be extremely challenging. Glomus yugular pdf glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma. Current perspectives in the management of glomus jugulare tumors narayan. The area of the skull affected by this type of tumor is called the jugular foramen. Stereotactic linacradiosurgery for glomus jugulare tumors. Distinguishing these tumors can typically be done through a detailed ear microscope exam or with a magnetic resonance imaging mri or computed tomography ct scan.
The tissue comprising the glomus jugulare lies in the adventitia of the dome of the jugular bulb, as well as within the temporal bone. Glomus juglare tumor, case study and bibliographic reference. Glomus vagale tumor is a type of paraganglioma, which is a tumor that develops in the paraganglia a group of cells that are found near nerve cell bunches called ganglia. The classic manifestation of a carotid body tumor is a nontender, enlarging lateral neck mass which is mobile, pulsatile, and associated with a bruit. Glomus vagale tumors, specifically, grow in the paraganglia located near the vagus nerve, an important cranial nerve which serves many functions including empowering the vocal cords and the muscles of swallo. A glomus jugulare tumor is a tumor of the part of the temporal bone in the skull that involves the middle and inner ear structures. The overall mortality rate is worse for patients treated with radiotherapy although radiotherapy patients are higherrisk patients at the outset. Radiotherapy for glomus jugulare paraganglioma sciencedirect. The effectiveness of surgery compared with radiotherapy as the primary treatment for glomus jugulare tumors remains controversial. Summary the glomus juglare tumors are very uncommon. It should not be confused with paraganglioma, which were once called glomus tumour.
Glomus tumors affect females more often than males, and most patients are in their 40s or 50s at the time of. Pdf efficacy and safety of stereotactic radiosurgery for. Glomus tumors are classified into types depending on where they begin to grow. Symptoms of these tumors usually include pulsatile tinnitus, hearing loss, facial nerve paralysis, vertigo, otalgia, dysphagia, hoarseness, throat sore, episodic hypertension with headaches, and tachycardia. Jensen, md assistant professor, department of anesthesiology, university of iowa address correspondence to dr. Glomus jugulare jugular foramen paraganglioma, temporal bone paraganglioma, glomus tumor is a slow growing vascular tumor located at the skull base.
A paraganglioma is a rare neuroendocrine neoplasm that may develop at various body sites including the head, neck, thorax and abdomen. A rare case of glomus jugulare tumor presenting as. Associated with tiny nerves which exit the skull adjacent to the carotid artery and internal jugular vein are tiny groups of cells called paraganglia. This tumor gets its name from the nerves, called glomus bodies, and their location in a small opening in the temporal bone, known as the jugulare. May 12, 2019 glomus yugular timpanico pdf glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma.
The jugulare and tympanicum tumors commonly cause pulsatile tinnitus and hearing loss and may cause cranial. There is a high morbidity associated with surgical resection of glomus jugulare. Glomus tumors paraganglioma university of delaware. Mar 18, 2020 glomus yugular pdf glomus tumor was also the name formerly and incorrectly used for a tumor now called a paraganglioma.
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